A 55-year-old woman with hereditary haemorrhagic telangiectasia (HHT) underwent a left lateral liver bisegmentectomy (removal of segments 2 and 3) for hepatic-based arteriovenous malformations. This lesion determined a progressive fatigue and invalidating effort dyspnoea. The postoperative course was uneventful and the patient is currently doing well at 4 years after surgery. To our knowledge, this is the first case of hepatic-based HHT treated with liver resection. This anecdotal report should promote the evaluation of this approach in order to define its role in the treatment of liver involvement in this rare disease.

Orlando, G., Sabba, C., Carino, N., Scelzo, C., Tariciotti, L., Bonanni, L., et al. (2008). Non-transplant surgical approach to liver-based hereditary haemorrhagic telangiectasia: a first report. LIVER INTERNATIONAL, 28(4), 574-577 [10.1111/j.1478-3231.2007.01588.x].

Non-transplant surgical approach to liver-based hereditary haemorrhagic telangiectasia: a first report

BAIOCCHI, LEONARDO;TISONE, GIUSEPPE
2008

Abstract

A 55-year-old woman with hereditary haemorrhagic telangiectasia (HHT) underwent a left lateral liver bisegmentectomy (removal of segments 2 and 3) for hepatic-based arteriovenous malformations. This lesion determined a progressive fatigue and invalidating effort dyspnoea. The postoperative course was uneventful and the patient is currently doing well at 4 years after surgery. To our knowledge, this is the first case of hepatic-based HHT treated with liver resection. This anecdotal report should promote the evaluation of this approach in order to define its role in the treatment of liver involvement in this rare disease.
Pubblicato
Rilevanza internazionale
Articolo
Sì, ma tipo non specificato
Settore MED/12 - Gastroenterologia
Settore MED/18 - Chirurgia Generale
English
Con Impact Factor ISI
Arterovenous malformation; Hepatic resection; Hereditary haemorrhagic telangiectasia; Left-to-right shunt
adult; anamnesis; arteriovenous malformation; article; case report; computer assisted tomography; dyspnea; fatigue; female; follow up; hospital discharge; human; laparotomy; liver resection; liver surgery; liver transplantation; patient referral; physical examination; postoperative period; Rendu Osler Weber disease; surgical approach; symptom; Female; Follow-Up Studies; Hepatectomy; Humans; Middle Aged; Risk Assessment; Severity of Illness Index; Telangiectasia, Hereditary Hemorrhagic; Time Factors; Treatment Outcome
Orlando, G., Sabba, C., Carino, N., Scelzo, C., Tariciotti, L., Bonanni, L., et al. (2008). Non-transplant surgical approach to liver-based hereditary haemorrhagic telangiectasia: a first report. LIVER INTERNATIONAL, 28(4), 574-577 [10.1111/j.1478-3231.2007.01588.x].
Orlando, G; Sabba, C; Carino, Ndl; Scelzo, C; Tariciotti, L; Bonanni, L; Angelo, M; Baiocchi, L; Lerut, J; Tisone, G
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Utilizza questo identificativo per citare o creare un link a questo documento: http://hdl.handle.net/2108/57929
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