We describe a 7-year-old patient with autism, moderate mental retardation, secondary microcephaly, agenesis of right optic nerve, and dysmorphic features carrying a de novo cryptic deletion of chromosome 2p25.2, detected by aCGH. Pure monosomies of 2p are very rare, and are usually observed as part of more complex aberrations involving other chromosomes. To the best of our knowledge, this is the first case presenting with a severe clinical phenotype and a de novo pure deletion of 2p25.2. The phenotypic effects of this rearrangement and the role of SOX11 gene, removed in our case, are herein discussed.

Lo Castro, A., Giana, G., Fichera, M., Castiglia, L., Grillo, L., Musumeci, S., et al. (2009). Deletion 2p25.2: a cryptic chromosome abnormality in a patient with autism and mental retardation detected using aCGH. EUROPEAN JOURNAL OF MEDICAL GENETICS, 52(1), 67-70 [10.1016/j.ejmg.2008.09.004].

Deletion 2p25.2: a cryptic chromosome abnormality in a patient with autism and mental retardation detected using aCGH

GALASSO, CINZIA;CURATOLO, PAOLO
2009-02-01

Abstract

We describe a 7-year-old patient with autism, moderate mental retardation, secondary microcephaly, agenesis of right optic nerve, and dysmorphic features carrying a de novo cryptic deletion of chromosome 2p25.2, detected by aCGH. Pure monosomies of 2p are very rare, and are usually observed as part of more complex aberrations involving other chromosomes. To the best of our knowledge, this is the first case presenting with a severe clinical phenotype and a de novo pure deletion of 2p25.2. The phenotypic effects of this rearrangement and the role of SOX11 gene, removed in our case, are herein discussed.
feb-2009
Pubblicato
Rilevanza internazionale
Articolo
Sì, ma tipo non specificato
Settore MED/39 - NEUROPSICHIATRIA INFANTILE
English
Con Impact Factor ISI
Lo Castro, A., Giana, G., Fichera, M., Castiglia, L., Grillo, L., Musumeci, S., et al. (2009). Deletion 2p25.2: a cryptic chromosome abnormality in a patient with autism and mental retardation detected using aCGH. EUROPEAN JOURNAL OF MEDICAL GENETICS, 52(1), 67-70 [10.1016/j.ejmg.2008.09.004].
Lo Castro, A; Giana, G; Fichera, M; Castiglia, L; Grillo, L; Musumeci, S; Galasso, C; Curatolo, P
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2108/45170
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