X-linked agammaglobulinemia is an inherited immunodeficiency recognized since 1952. In spite of seven decades of experience, there is still a limited understanding of regional differences in presentation and complications. This study was designed by the Primary Immunodeficiencies Committee of the World Allergy Organization to better understand regional needs, challenges and unique patient features.

El-Sayed, Z.a., Abramova, I., Aldave, J.c., Al-Herz, W., Bezrodnik, L., Boukari, R., et al. (2019). X-linked agammaglobulinemia (XLA):Phenotype, diagnosis, and therapeutic challenges around the world. THE WORLD ALLERGY ORGANIZATION JOURNAL, 12(3), 100018 [10.1016/j.waojou.2019.100018].

X-linked agammaglobulinemia (XLA):Phenotype, diagnosis, and therapeutic challenges around the world

Cancrini C.;Moschese V.;
2019-01-01

Abstract

X-linked agammaglobulinemia is an inherited immunodeficiency recognized since 1952. In spite of seven decades of experience, there is still a limited understanding of regional differences in presentation and complications. This study was designed by the Primary Immunodeficiencies Committee of the World Allergy Organization to better understand regional needs, challenges and unique patient features.
2019
Pubblicato
Rilevanza internazionale
Articolo
Esperti anonimi
Settore MED/38 - PEDIATRIA GENERALE E SPECIALISTICA
English
Con Impact Factor ISI
Agammaglobulinemia; Autoimmunity; CLD, Chronic lung disease; FH, Family history; GI, Gastrointestinal; Immunoglobulin; Infection; JIA, juvenile idiopathic arthritis; Outcomes; SCIG, Subcutaneous immunoglobulin; Therapy; VAPP, Vaccine associated paralytic poliomyelitis; XLA; XLA, X-linked agammaglobulinemia
El-Sayed, Z.a., Abramova, I., Aldave, J.c., Al-Herz, W., Bezrodnik, L., Boukari, R., et al. (2019). X-linked agammaglobulinemia (XLA):Phenotype, diagnosis, and therapeutic challenges around the world. THE WORLD ALLERGY ORGANIZATION JOURNAL, 12(3), 100018 [10.1016/j.waojou.2019.100018].
El-Sayed, Za; Abramova, I; Aldave, Jc; Al-Herz, W; Bezrodnik, L; Boukari, R; Bousfiha, Aa; Cancrini, C; Condino-Neto, A; Dbaibo, G; Derfalvi, B; Dogu,...espandi
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2108/217627
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