Myotonic dystrophy type 1 (DM1), the most common muscular dystrophy observed in adults, is a genetic multisystem disorder affecting several other organs besides skeletal muscle, including the brain. Cognitive and personality abnormalities have been reported; however, no studies have investigated brain functional networks and their relationship with personality traits/disorders in patients with DM1.

Serra, L., Silvestri, G., Petrucci, A., Basile, B., Masciullo, M., Makovac, E., et al. (2014). Abnormal functional brain connectivity and personality traits in myotonic dystrophy type 1, 71(5), 603-611 [10.1001/jamaneurol.2014.130].

Abnormal functional brain connectivity and personality traits in myotonic dystrophy type 1

CALTAGIRONE, CARLO;
2014-05-01

Abstract

Myotonic dystrophy type 1 (DM1), the most common muscular dystrophy observed in adults, is a genetic multisystem disorder affecting several other organs besides skeletal muscle, including the brain. Cognitive and personality abnormalities have been reported; however, no studies have investigated brain functional networks and their relationship with personality traits/disorders in patients with DM1.
mag-2014
Pubblicato
Rilevanza internazionale
Articolo
Esperti anonimi
Settore MED/26 - NEUROLOGIA
English
Magnetic Resonance Imaging; Humans; Myotonic Dystrophy; Cohort Studies; Adult; Brain; Personality; Middle Aged; Personality Inventory; Nerve Net; Male; Female
Serra, L., Silvestri, G., Petrucci, A., Basile, B., Masciullo, M., Makovac, E., et al. (2014). Abnormal functional brain connectivity and personality traits in myotonic dystrophy type 1, 71(5), 603-611 [10.1001/jamaneurol.2014.130].
Serra, L; Silvestri, G; Petrucci, A; Basile, B; Masciullo, M; Makovac, E; Torso, M; Spanò, B; Mastropasqua, C; Harrison, N; Bianchi, M; Giacanelli, M; Caltagirone, C; Cercignani, M; Bozzali, M
Articolo su rivista
File in questo prodotto:
Non ci sono file associati a questo prodotto.

I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2108/88431
Citazioni
  • ???jsp.display-item.citation.pmc??? ND
  • Scopus 61
  • ???jsp.display-item.citation.isi??? 54
social impact