A rare but fatal behçet variant: the hughes–stovin syndrome—successful case report and new evidence from literature review

hughes-stovin syndrome (HSS) is a rare potentially fatal vasculitis supposedly belonging to the spectrum of behçet disease without ocular involvement. HSS tends to play by a temporal pattern, starting with thrombosis and followed by formation of pulmonary aneurysms. wince its mortality can reach 25% of cases, early recognition and appropriate therapy represent the major clinical challenges. we describe a rare case of HSS successfully treated via multidisciplinary management by an endovascular approach and immunosuppressive therapy.