A case of a 37-year old man affected by tuberous sclerosis with bilateral renal angiomyolipomas is described. This is a very important association since it is observed in 20 to 50% of cases of tuberous sclerosis. Like other neurocutaneous syndromes, tuberous sclerosis can predispose to the onset of several benign and malignant neoplasms such as cardiac rabdomyosarcomas, glial tumours and renal angiomyolipomas.

Nini, G., Iraci, S., Bianchi, L., Marinaro, C., Angelini, E. (1993). Tuberous sclerosis with specific renal involvement. ANNALI ITALIANI DI DERMATOLOGIA CLINICA E SPERIMENTALE, 47(2), 165-168.

Tuberous sclerosis with specific renal involvement

BIANCHI, LUCA;
1993-01-01

Abstract

A case of a 37-year old man affected by tuberous sclerosis with bilateral renal angiomyolipomas is described. This is a very important association since it is observed in 20 to 50% of cases of tuberous sclerosis. Like other neurocutaneous syndromes, tuberous sclerosis can predispose to the onset of several benign and malignant neoplasms such as cardiac rabdomyosarcomas, glial tumours and renal angiomyolipomas.
1993
Pubblicato
Rilevanza nazionale
Articolo
Sì, ma tipo non specificato
Settore MED/35 - MALATTIE CUTANEE E VENEREE
Italian
Senza Impact Factor ISI
case report; renal angiomyolipoma; tuberous sclerosis; adult; angiomyolipoma; article; case report; human; human tissue; male; tuberous sclerosis
Nini, G., Iraci, S., Bianchi, L., Marinaro, C., Angelini, E. (1993). Tuberous sclerosis with specific renal involvement. ANNALI ITALIANI DI DERMATOLOGIA CLINICA E SPERIMENTALE, 47(2), 165-168.
Nini, G; Iraci, S; Bianchi, L; Marinaro, C; Angelini, E
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2108/57372
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