Congenital intrahepatic portosystemic shunts are rare hepatic vascular anomalies that often lead to severe secondary conditions. A 6-year-old boy was referred for assessment of severe hypoxia, and a large liver mass was diagnosed with such a malformation and was managed by direct closure of the venous fistula by interventional radiology. Follow-up assessment shows normalization of the respiratory condition and a progressive reduction of the vascular liver lesion. Review of literature suggests that radiologic interventions are currently the criterion standard for managing these conditions, with surgery reserved for patients who are not eligible for radiologic procedure and those requiring liver transplantation.
Grimaldi, C., Monti, L., Falappa, P., D'Ambrosio, G., Manca, A., DE VILLE DE GOYET, J. (2012). Congenital intrahepatic portohepatic shunt managed by interventional radiologic occlusion: a case report and literature review. JOURNAL OF PEDIATRIC SURGERY, 47(2), e27-e31 [10.1016/j.jpedsurg.2011.10.079].
Congenital intrahepatic portohepatic shunt managed by interventional radiologic occlusion: a case report and literature review
DE VILLE DE GOYET, JEAN
2012-02-01
Abstract
Congenital intrahepatic portosystemic shunts are rare hepatic vascular anomalies that often lead to severe secondary conditions. A 6-year-old boy was referred for assessment of severe hypoxia, and a large liver mass was diagnosed with such a malformation and was managed by direct closure of the venous fistula by interventional radiology. Follow-up assessment shows normalization of the respiratory condition and a progressive reduction of the vascular liver lesion. Review of literature suggests that radiologic interventions are currently the criterion standard for managing these conditions, with surgery reserved for patients who are not eligible for radiologic procedure and those requiring liver transplantation.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
